RECURRENT PSEUDO-OBSTRUCTION OF THE LARGE BOWEL ASSOCIATED WITH SANJAD-SAKATI SYNDROME: A CASE REPORT

Sanjad-Sakati Syndrome, also referred to as Hypoparathyroidism-Retardation-Dysmorphism Syndrome or Middle East was first reported in Saudi Arabia 1988 and later a definitive report by (Sanjad et al.) 1991. It is rare autosomal recessive condition almost exclusively the Arab population. The characterized an extensive array of symptoms, including congenital hypoparathyroidism, severe growth developmental retardation both intrauterine post-natal, low Intelligence, seizures, distinctive facial characteristics. We present incidence this disease repeated pseudo-obstruction. Electrolyte metabolic disturbances, which are cause pseudo-obstruction intestine child, must be evaluated order avoid unnecessary surgical intervention, may prove life threatening.